Long-term evaluation of Cochlear implantation in Cogan syndrome.
PMID 20798564 · ORL; journal for oto-rhino-laryngology and its related specialties · 2010 · DOI 10.1159/000318870
Authors: Georgios Kontorinis; Alexandros Giourgas; Juergen Neuburger; Anke Lesinski-Schiedat; Thomas Lenarz
Abstract
The evaluation of long-term results of cochlear implantation in patients with typical Cogan syndrome. The medical records of approximately 3,000 patients who underwent cochlear implantation in a tertiary centre within the period 1992-2007 were retrospectively examined. Four cochlear implant recipients with Cogan syndrome (6 implantations) were identified. One cochlea was found to be partially obliterated; the electrode could, however, be completely inserted. Wound healing disorders and infections in a patient with systemic symptoms were the only postoperative complications. Hearing outcome was favorable, with average HSM and monosyllabic scores of 96.7 and 82.5%, respectively, in an average follow-up time of 9.25 years. Cochlear implantation is the appropriate hearing rehabilitation method in Cogan syndrome patients. Although the basic illness does not affect the long-term hearing outcome, skin-atrophy-related complications in cases with systemic symptoms may occur. Finally, the cochlear implant surgeon should be aware of the possible cochlea obliteration.
Adult; Child; Cochlear Implantation; Cogan Syndrome; Deafness; Female; Follow-Up Studies; Humans; Retrospective Studies; Time Factors; Treatment Outcome; Young Adult
Cite
Georgios Kontorinis; Alexandros Giourgas; Juergen Neuburger; Anke Lesinski-Schiedat; Thomas Lenarz. Long-term evaluation of Cochlear implantation in Cogan syndrome. ORL; journal for oto-rhino-laryngology and its related specialties (2010). PMID 20798564. DOI 10.1159/000318870.